Ichthyosis overview and Classification

Ichthyosis, is a common genetic skin disease keratosis, formerly ichthyosis, the Chinese said Chipi ringworm. Mainly for the limbs or trunk extensor side of the skin dry, rough diamond or polygonal Linxie with appearance-such as Chipi Yulinzhuang or because of different genetic pattern can be divided into autosomal dominant inheritance of ichthyosis unusual, X-linked ichthyosis of unusual, congenital ichthyosis kind of red and lamellar ichthyosis.
Ichthyosis by signs and symptoms can be divided into four types: 1. Dominant unusual type ichthyosis (1) after birth in March to five between the incidence; (2) dry skin, to short covering gray or brown diamond-shaped polygon Linxie, peripheral Qiaoqi, the central keep skin; (3) distribution in the limbs, the main extensor side of the back; 2. Unusual type of the disease ichthyosis (1) Date of birth within three months after the onset, the only male involvement; (2) Thick skin drying, the overlying Linxie large and dark brown, winter-summer light. Increase with age, the same damage, and even intensified; (3) Distribution of lesions body to, side, ears, neck involvement the most important. Qu side often involved. 3. Congenital ichthyosis kind of red (1) at the time of birth body that is armor-like multi-Lin Xie, after shedding wet rough surface, there are relaxation of the cell; (2) was serious Hand, Foot and claw-shaped; (3) autosomal dominant inheritance. 4. Layer plate ichthyosis (1) systemic baby after birth fire for a wide range of cotton wrapped tightly rubbery membrane, the membrane shedding a few days later, extensive skin flushing, and there are large polyhedrosis Lin Xie, the Central adhesive edge free; (2) palmoplantar hyperkeratosis, fingernails and excessive hair growth; (3) 2 / 3 of patients have eyelid valgus.