Dandy-Walker syndrome

Overview said, Dandy-Walker malformation; Fourth ventricle Kong obliterans syndrome; Non-communicating hydrocephalus. Cause pathogenesis fourth ventricle or adjacent to the middle Kong Kong congenital fiber network, with fiber or cyst occlusion; cisternals was congenital cerebral meningocele, cerebellum or ectopic meningeal infection by blocking adhesion, and the midline posterior fossa tumors can cause varying degrees of hydrocephalus. Clinical manifestations Dandy-Walker malformation more than six months after the brain symptoms of hydrocephalus symptoms of increased intracranial pressure and , the symptoms can also be associated with cerebellar and cranial nerve palsy symptoms. Acquired obstruction was particularly prevalent in the posterior fossa tumors, sexual performance for the increased intracranial pressure symptoms, the symptoms and cerebellar damage to the cranial nerve symptoms. CT can be seen above 4 intraventricular symmetry of the ventricular system expansion, brain edema and posterior fossa occupying signs. Differential diagnosis (1) congenital dysplasia (congenital aplasia), including 4 intraventricular mesoporous or occlusion of the lateral hole or four brain cyst formation, signs of the disease hydrocephalus than infants can be seen, performance of the skull for increased, and the Hang night closed doors or expanded, bone joints separated from the patient performance howling, irritability, even convulsions such as ventilation. CT images alone, it is difficult to differentiate between Room Kong or cyst blocked, and need to rely on the identification of ventricular angiography. The former indoor cerebral angiography were filling agent, the latter within the cyst without contrast agent into the filling defect and the situation was. Whether due to the occlusion of what should be the appropriate surgical treatment as early as possible. (2) 4 intraventricular cysticercosis occlusion multiple brain cysticercosis is very easy diagnosis, a single-ventricle diagnosis difficult. 4 intraventricular cystic carinii formed, and the fourth ventricle congenital cyst formation is difficult to distinguish, But the former "pork meters" food history and tapeworm proglottis emit history, blood HIA more positive. Anti-brain cysticercosis water treatment can alleviate or disappeared. (3) posterior fossa tumors (tumor of posterior cranial fossa) Line tumor with hydrocephalus occurred earlier in medulloblastoma, Angioreticuloma and ependymal papilloma styles. Cerebellar hemisphere and the cerebellopontine angle tumors in advanced hydrocephalus there. Apart from a cerebral edema, there cerebellar symptoms and cranial nerve palsy symptoms, compression and displacement of the fourth ventricle or occlusion. (4) midbrain or deformities caused by inflammatory adhesion hydrocephalus only see the third ventricle and lateral ventricles expand, and the fourth ventricle normal. Communicating hydrocephalus ventricle, the basal cistern and subarachnoid spider is expanding.