Morvan's syndrome

Has outlined the use of this name, and more use of syringomyelia associated with the upper extremity acromegaly malnutrition or hereditary sensory nerve root disease caused by the lower limbs broken toe syndrome. Cause pathogenesis of common diseases because of syringomyelia, the Ma-year-old neuritis, diabetes neuritis, hereditary sensory nerve root disease, Children feel such neuritis. On the pathogenesis, some people think that the loss due to pain after repeated caused the burns and trauma; Some people believe that the autonomic nervous system, autonomic obstacles, because external stimuli, cause sweating and vasomotor dysfunction regulation produce ischemia, bleeding, edema and necrosis; In addition, autonomic also direct the nutrition factor, the lack of necrosis after lead. Clinical features of the limb paralysis, sensory dysfunction, the finger (toe) painless necrosis. 11-30-year-old disease, the rapid onset implicit attack. The most common neck injury, the performance of the unilateral finger numbness, pain and temperature sense partial failures, the tactile feel and deep, Lesions from the side of the chest and upper arm to the development of bilateral and finally hand weakness and atrophy, deformation-shaped, deep reflection disappeared, neck stiffness, strong spontaneous pain. Medullary damage involving the face, waist and leg damage involved with pots. Found lesions regional pain barriers, obstacles and nutrition ulcers, muscle atrophy and spontaneous contraction, ataxia, may have Charcot's joint, neurogenic bladder, it is common to Horner's syndrome. Differential diagnosis (1) syringomyelia (symptom) is a slow progress in the spinal cord and ( or) the medulla degeneration. Age of onset is usually between 20 to 30 years of age, clinical features of the damaged section of the separation barrier feeling, lower motor neuron obstacles, Beam long conduction dysfunction and nutrition obstacles. Slow disease progression, the earliest symptoms showed segmental distribution, the first affected arm. CT and MRI can clearly diagnose, especially MRI is the most effective diagnostic method. (2) of leprosy neuritis (leprosis neuritis) in allergic leprosy or tuberculosis often-aggression guilty of peripheral nerve. Slow onset, regional nerve damage pain, temporary hypersensitivity. Severe itching, following a "gloves-socks" type or segmental distribution of sensory loss. Distal limb muscle weakness and atrophy, tendon reflexes diminish or disappear, or hand-shaped pedal. By V, vii cranial nerve damage caused facial paralysis or feeling of loss is also common. physically autonomic dysfunction and nutrition obvious obstacles. Peripheral nerve thick as strong cords to the ulnar nerve and nerve shallow support the most vulnerable and touched. Nasal found acid-fast bacilli can be diagnosed and, if necessary, the nerve biopsy suspicious lesions to help diagnosis. (3) diabetic neuropathy (diabetic neuropathy) and diabetes right around the center Nerve damage can be caused, but the damage was mostly around, more common in the distal extremities (particularly lower limb), mostly females, There are many clinical types. Sensory neuropathy-numbness of the distal limb numbness symmetry, the ants go flu abnormal feeling Pain-acromegaly was spontaneous burning, lightning-like pain, or two-coexist. If combined with decreased muscle strength and muscle atrophy claimed sensory-motor polyneuropathy. Plant neuropathy common pupil and lacrimal gland secretion of obstacles, cardiovascular, gastrointestinal tract, Genitourinary and sweat secretion disorders. This merger of three multi-Morvan's syndrome. (4) hereditary sensory nerve neuropathy (hereditary sensory radicula r neuropathy) is the disease most often autosomal dominant inheritance. Usually in the 20 - 30-year-old, and occasionally children onset, the most prominent symptoms of plantar pressure were recurring ulcers, The earliest symptoms often for the first metatarsal head plantar skin black scab, bed rest can heal, but Shimoji activities recurrence. Loss of sensation in a "Watao" type, with the most serious limb distal to the proximal gradually transferred to normal, Foot and lower leg pain in the skin temperature Cox and Fine identify McGREGOR may completely disappear.